{"id":11901,"date":"2025-06-17T15:01:38","date_gmt":"2025-06-17T13:01:38","guid":{"rendered":"https:\/\/valintermed.com\/?p=11901"},"modified":"2025-06-17T15:01:38","modified_gmt":"2025-06-17T13:01:38","slug":"plastinchatyy-ihtioz","status":"publish","type":"post","link":"https:\/\/valintermed.com\/en\/medlibrary\/plastic-surgery\/","title":{"rendered":"Lamellar ichthyosis"},"content":{"rendered":"
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Lamellar ichthyosis is a rare hereditary skin disease of an autosomal recessive type, characterized by pronounced hyperkeratosis and a violation of the processes of keratinization of the epidermis. With this dermatosis, massive peeling of the skin in large plates resembling fish scales is observed, which determined the name of the pathology. The disease manifests itself immediately after birth, when the newborn is covered with a kind of colloidal film, which subsequently transforms into pronounced lamellar desquamation. The pathogenesis of the disease is associated with a violation of the barrier function of the skin and keratinocyte processes, which leads to a significant loss of fluid through the skin and increased sensitivity to infectious agents.<\/p>\n

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