{"id":11797,"date":"2025-07-26T00:58:08","date_gmt":"2025-07-25T22:58:08","guid":{"rendered":"https:\/\/valintermed.com\/?p=11797"},"modified":"2025-07-26T00:58:08","modified_gmt":"2025-07-25T22:58:08","slug":"soedinitelnyy-bullyoznyy-epidermoliz","status":"publish","type":"post","link":"https:\/\/valintermed.com\/en\/medlibrary\/conjugate-bullous-epidermal-necrosis\/","title":{"rendered":"Junctional epidermolysis bullosa"},"content":{"rendered":"
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Junctional epidermolysis bullosa (JBE) is a genetic disorder characterized by increased fragility of the skin and the formation of blisters that occur under the influence of mechanical pressure or friction. The pathology is associated with disorders in the structures of connective tissue, which leads to destabilization and disruption of the integrity of the epidermis. The main clinical manifestations of JBE are blisters, flakes and erosions on the skin, especially in areas subject to abrasion. Skin lesions can be accompanied by pain, swelling and skin resurfacing, which significantly worsens the quality of life of patients. There are various forms of epidermolysis, each of which has its own patterns and features. Thus, JBE requires an integrated approach to diagnosis and treatment aimed at managing symptoms and reducing the risk of complications.<\/p>\n

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